DeMartino et al. (2016) report the case of a non-smoking 38-year-old man with obesity, hypertension and hyperlipidemia and a history of recurrent pneumothoraces over the past 9 years. The patient had no pneumothorax on his family history. Skin exams showed thorascostomy scars and numerous follicularbased white papules on the face and neck. CT scans detected multiple cysts on both lungs but no renal lesions. Histology analysis found dermal follicular structures with perifollicular and increased dermal, consistent with the fibrofolliculomas of Birt-Hogg-Dubé (BHD).