Tellechea et al., (2015) review the development of hair follicles and the classification of benign hair follicle tumours (BHFT). Different BHFT histologies are discussed including differential diagnoses for each; trichodiscomas and fibrofolliculomas are both discussed as a marker of BHD. Awareness of these different cutaneous lesions allows dermatologists to identify patients who may be carrying mutations associated with cancer-prone syndromes.